Giant recurrent infantile myofibromatosis of the leg in a 3 year-old
نویسندگان
چکیده
منابع مشابه
Infantile myofibromatosis*
Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.
متن کاملInfantile Myofibromatosis
Infantile myofibromatosis (IMP) is a rare tumour with a wide spectrum of disease activity ra a solitarY cutaneous nodule through to a multicentric form ,vith widespread visceral involveluent. R is charactelised by its unique ability to spontaneously regress and has a typical histological appearance of a~tin-positivefibroblasts arranged in whorls or fascicles and vessels in a pericytomatous patt...
متن کاملInfantile myofibromatosis.
Infantile myofibromatosis (IMF) is a rare tumour with a wide spectrum of disease activity ranging from a solitary cutaneous nodule through to a multicentric form with widespread visceral involvement. It is characterised by its unique ability to spontaneously regress and has a typical histological appearance of actin-positive fibroblasts arranged in whorls or fascicles and vessels in a pericytom...
متن کاملChronic Recurrent Multifocal Osteomyelitis in a 9-year-old Boy
Chronic recurrent multifocal osteomyelitis (CRMO) is a rare aseptic, auto-inflammatory bone disorder. CRMO presents with bone pain with or without fever. The diagnosis of CRMO is a diagnosis of exclusion and should be included in the differential diagnosis of chronic inflammatory bone lesions in children. Cultures of the bone are typically sterile, antibiotic therapy does not result in clinic...
متن کاملMulticentric Infantile Myofibromatosis
We present a case of multicentric infantile myofibromatosis in a 3-month-old male infant who had multiple papular lesions on his extremities and trunk and a slowly growing and bulging mass on his left occipital area since birth. His general physical condition was good and psychomotor development was normal. The diagnosis was established by histopathological and immunohistochemical studies along...
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ژورنال
عنوان ژورنال: African Journal of Paediatric Surgery
سال: 2009
ISSN: 0189-6725
DOI: 10.4103/0189-6725.48579